Photo of Professor Kevin Southern

Professor Kevin Southern MBChB, MRCP, FRCPCH, PhD

Professor of Child Health Women's & Children's Health

    Publications

    2021

    Process evaluation of co-designed interventions to improve communication of positive newborn bloodspot screening results (Journal article)

    Chudleigh, J., Holder, P., Moody, L., Simpson, A., Southern, K., Morris, S., . . . Olander, E. (2021). Process evaluation of co-designed interventions to improve communication of positive newborn bloodspot screening results. BMJ OPEN, 11(8). doi:10.1136/bmjopen-2021-050773

    DOI: 10.1136/bmjopen-2021-050773

    A systematic cochrane review of corrector therapies (with or without potentiators) for people with cystic fibrosis with class II gene variants (most commonly F508DEL). (Journal article)

    Southern, K. W., Murphy, J., Sinha, I. P., & Nevitt, S. J. (n.d.). A systematic cochrane review of corrector therapies (with or without potentiators) for people with cystic fibrosis with class II gene variants (most commonly F508DEL).. Paediatric respiratory reviews. doi:10.1016/j.prrv.2021.03.001

    DOI: 10.1016/j.prrv.2021.03.001

    A survey of the prevalence, management and outcome of infants with an inconclusive diagnosis following newborn bloodspot screening for cystic fibrosis (CRMS/CFSPID) in six Italian centres. (Journal article)

    Terlizzi, V., Claut, L., Tosco, A., Colombo, C., Raia, V., Fabrizzi, B., . . . Padoan, R. (2021). A survey of the prevalence, management and outcome of infants with an inconclusive diagnosis following newborn bloodspot screening for cystic fibrosis (CRMS/CFSPID) in six Italian centres.. Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society. doi:10.1016/j.jcf.2021.03.015

    DOI: 10.1016/j.jcf.2021.03.015

    Transmission, adaptation and geographical spread of the Pseudomonas aeruginosa Liverpool epidemic strain (Journal article)

    Moore, M. P., Lamont, I. L., Williams, D., Paterson, S., Kukavica-Ibrulj, I., Tucker, N. P., . . . Winstanley, C. (2021). Transmission, adaptation and geographical spread of the Pseudomonas aeruginosa Liverpool epidemic strain. MICROBIAL GENOMICS, 7(3). doi:10.1099/mgen.0.000511

    DOI: 10.1099/mgen.0.000511

    Cystic fibrosis newborn screening: the importance of bloodspot sample quality (Journal article)

    Doull, I., Course, C. W., Hanks, R. E., Southern, K. W., Forton, J. T., Thia, L. P., & Moat, S. J. (2021). Cystic fibrosis newborn screening: the importance of bloodspot sample quality. ARCHIVES OF DISEASE IN CHILDHOOD, 106(3), 253-257. doi:10.1136/archdischild-2020-318999

    DOI: 10.1136/archdischild-2020-318999

    Defining key outcomes to evaluate performance of newborn screening programmes for cystic fibrosis. (Journal article)

    Munck, A., Southern, K. W., Castellani, C., de Winter-de Groot, K. M., Gartner, S., Kashirskaya, N., . . . European CF Society Neonatal Screening Working Group (ECFS NSWG). (2021). Defining key outcomes to evaluate performance of newborn screening programmes for cystic fibrosis.. Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society. doi:10.1016/j.jcf.2021.02.006

    DOI: 10.1016/j.jcf.2021.02.006

    2020

    Corrector therapies (with or without potentiators) for people with cystic fibrosis with class II CFTR gene variants (most commonly F508del) (Journal article)

    Southern, K. W., Murphy, J., Sinha, I. P., & Nevitt, S. J. (2020). Corrector therapies (with or without potentiators) for people with cystic fibrosis with class II CFTR gene variants (most commonly F508del). COCHRANE DATABASE OF SYSTEMATIC REVIEWS, (12). doi:10.1002/14651858.CD010966.pub3

    DOI: 10.1002/14651858.CD010966.pub3

    Processing of positive newborn screening results: a qualitative exploration of current practice in England (Journal article)

    Chudleigh, J., Chinnery, H., Holder, P., Carling, R. S., Southern, K., Olander, E., . . . Simpson, A. (2020). Processing of positive newborn screening results: a qualitative exploration of current practice in England. BMJ OPEN, 10(12). doi:10.1136/bmjopen-2020-044755

    DOI: 10.1136/bmjopen-2020-044755

    Updated guidance on the management of children with cystic fibrosis transmembrane conductance regulator-related metabolic syndrome/cystic fibrosis screen positive, inconclusive diagnosis (CRMS/CFSPID). (Journal article)

    Barben, J., Castellani, C., Munck, A., Davies, J. C., de Winter-de Groot, K. M., Gartner, S., . . . European CF Society Neonatal Screening Working Group (ECFS NSWG). (2020). Updated guidance on the management of children with cystic fibrosis transmembrane conductance regulator-related metabolic syndrome/cystic fibrosis screen positive, inconclusive diagnosis (CRMS/CFSPID).. Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society. doi:10.1016/j.jcf.2020.11.006

    DOI: 10.1016/j.jcf.2020.11.006

    Cystic fibrosis newborn screening for R117H in England (Conference Paper)

    Dafydd, C., Moat, S., Southern, K. W., & Doull, I. J. M. (2020). Cystic fibrosis newborn screening for R117H in England. In EUROPEAN RESPIRATORY JOURNAL Vol. 56. doi:10.1183/13993003.congress-2020.2762

    DOI: 10.1183/13993003.congress-2020.2762

    Should the D1152H variant be included in cystic fibrosis newborn screening programmes? (Conference Paper)

    Dafydd, C., Southern, K. W., Moat, S., & Doull, I. J. M. (2020). Should the D1152H variant be included in cystic fibrosis newborn screening programmes?. In EUROPEAN RESPIRATORY JOURNAL Vol. 56. doi:10.1183/13993003.congress-2020.2761

    DOI: 10.1183/13993003.congress-2020.2761

    Why Do We Screen Newborn Infants for Cystic Fibrosis? (Journal article)

    Barben, J., & Southern, K. W. (2020). Why Do We Screen Newborn Infants for Cystic Fibrosis?. International journal of neonatal screening, 6(3). doi:10.3390/ijns6030056

    DOI: 10.3390/ijns6030056

    Constructing a Bioethical Framework to Evaluate and Optimise Newborn Bloodspot Screening for Cystic Fibrosis (Journal article)

    Armstrong, R. E., Frith, L., Ulph, F. M., & Southern, K. W. (2020). Constructing a Bioethical Framework to Evaluate and Optimise Newborn Bloodspot Screening for Cystic Fibrosis. International Journal of Neonatal Screening, 6(2). doi:10.3390/ijns6020040

    DOI: 10.3390/ijns6020040

    COVID-19 infection in children (Journal article)

    Sinha, I. P., Harwood, R., Semple, M. G., Hawcutt, D. B., Thursfield, R., Narayan, O., . . . Southern, K. W. (2020). COVID-19 infection in children. LANCET RESPIRATORY MEDICINE, 8(5), 446-447. Retrieved from http://gateway.webofknowledge.com/

    Impact of COVID-19 on people with cystic fibrosis (Journal article)

    Colombo, C., Burgel, P. -R., Gartner, S., van Koningsbruggen-Rietschel, S., Naehrlich, L., Sermet-Gaudelus, I., & Southern, K. W. (2020). Impact of COVID-19 on people with cystic fibrosis. LANCET RESPIRATORY MEDICINE, 8(5), E35-E36. doi:10.1016/S2213-2600(20)30177-6

    DOI: 10.1016/S2213-2600(20)30177-6

    The future of cystic fibrosis care: a global perspective (Journal article)

    Bell, S. C., Mall, M. A., Gutierrez, H., Macek, M., Madge, S., Davies, J. C., . . . Ratjen, F. (2020). The future of cystic fibrosis care: a global perspective. LANCET RESPIRATORY MEDICINE, 8(1), 65-124. doi:10.1016/S2213-2600(19)30337-6

    DOI: 10.1016/S2213-2600(19)30337-6

    2019

    An open-label extension study of ivacaftor in children with CF and a CFTR gating mutation initiating treatment at age 2-5 years (KLIMB) (Journal article)

    Rosenfeld, M., Cunningham, S., Harris, W. T., Lapey, A., Regelmann, W. E., Sawicki, G. S., . . . Grp, K. L. I. M. B. S. (2019). An open-label extension study of ivacaftor in children with CF and a CFTR gating mutation initiating treatment at age 2-5 years (KLIMB). JOURNAL OF CYSTIC FIBROSIS, 18(6), 838-843. doi:10.1016/j.jcf.2019.03.009

    DOI: 10.1016/j.jcf.2019.03.009

    Inconclusive diagnosis after a positive newborn bloodspot screening result for cystic fibrosis; clarification of the harmonised international definition. (Journal article)

    Southern, K. W., Barben, J., Gartner, S., Munck, A., Castellani, C., Mayell, S. J., . . . Farrell, P. M. (2019). Inconclusive diagnosis after a positive newborn bloodspot screening result for cystic fibrosis; clarification of the harmonised international definition. JOURNAL OF CYSTIC FIBROSIS, 18(6), 778-780. doi:10.1016/j.jcf.2019.04.010

    DOI: 10.1016/j.jcf.2019.04.010

    Inhaled hypertonic saline for 3-6-year-olds with cystic fibrosis (Journal article)

    Southern, K. W., & Sinha, I. P. (2019). Inhaled hypertonic saline for 3-6-year-olds with cystic fibrosis. LANCET RESPIRATORY MEDICINE, 7(9), 730-732. doi:10.1016/S2213-2600(19)30183-3

    DOI: 10.1016/S2213-2600(19)30183-3

    International approaches for delivery of positive newborn bloodspot screening results for CF (Journal article)

    Chudleigh, J., Ren, C. L., Barben, J., & Southern, K. W. (2019). International approaches for delivery of positive newborn bloodspot screening results for CF. JOURNAL OF CYSTIC FIBROSIS, 18(5), 614-621. doi:10.1016/j.jcf.2019.04.004

    DOI: 10.1016/j.jcf.2019.04.004

    Psychological Impact on Parents of an Inconclusive Diagnosis Following Newborn Bloodspot Screening for Cystic Fibrosis: A Qualitative Study. (Journal article)

    Johnson, F., Southern, K. W., & Ulph, F. (2019). Psychological Impact on Parents of an Inconclusive Diagnosis Following Newborn Bloodspot Screening for Cystic Fibrosis: A Qualitative Study.. International journal of neonatal screening, 5(2), 23. doi:10.3390/ijns5020023

    DOI: 10.3390/ijns5020023

    Adherence to Aerosol Therapy in Young People With Cystic Fibrosis: Patient and Parent Perspectives Following Electronic Data Capture (Journal article)

    O'Toole, D. P. H., Latchford, G. J., Duff, A. J. A., Ball, R., McCormack, P., McNamara, P. S., . . . Southern, K. W. (2019). Adherence to Aerosol Therapy in Young People With Cystic Fibrosis: Patient and Parent Perspectives Following Electronic Data Capture. QUALITATIVE HEALTH RESEARCH, 29(6), 846-856. doi:10.1177/1049732318805754

    DOI: 10.1177/1049732318805754

    A systematic Cochrane Review of correctors (specific therapies for class II CFTR mutations) for cystic fibrosis [1] (Journal article)

    Southern, K. W., Patel, S., Sinha, I. P., & Nevitt, S. J. (2019). A systematic Cochrane Review of correctors (specific therapies for class II CFTR mutations) for cystic fibrosis [1]. PAEDIATRIC RESPIRATORY REVIEWS, 30, 25-26. doi:10.1016/j.prrv.2019.01.003

    DOI: 10.1016/j.prrv.2019.01.003

    Exercise versus airway clearance techniques for people with cystic fibrosis (Journal article)

    Patterson, K. D., Walsh, A., McCormack, P., & Southern, K. W. (n.d.). Exercise versus airway clearance techniques for people with cystic fibrosis. Cochrane Database of Systematic Reviews. doi:10.1002/14651858.cd013285

    DOI: 10.1002/14651858.cd013285

    The increasing challenge of genetic counseling for cystic fibrosis. (Journal article)

    Foil, K. E., Powers, A., Raraigh, K. S., Wallis, K., Southern, K. W., & Salinas, D. (2019). The increasing challenge of genetic counseling for cystic fibrosis. JOURNAL OF CYSTIC FIBROSIS, 18(2), 167-174. doi:10.1016/j.jcf.2018.11.014

    DOI: 10.1016/j.jcf.2018.11.014

    A systematic Cochrane Review of autogenic drainage (AD) for airway clearance in cystic fibrosis (Conference Paper)

    McCormack, P., Burnham, P., & Southern, K. W. (2019). A systematic Cochrane Review of autogenic drainage (AD) for airway clearance in cystic fibrosis. In PAEDIATRIC RESPIRATORY REVIEWS Vol. 29 (pp. 23-24). doi:10.1016/j.prrv.2018.06.002

    DOI: 10.1016/j.prrv.2018.06.002

    Potentiators (specific therapies for class III and IV mutations) for cystic fibrosis (Journal article)

    Skilton, M., Krishan, A., Patel, S., Sinha, I. P., & Southern, K. W. (2019). Potentiators (specific therapies for class III and IV mutations) for cystic fibrosis. COCHRANE DATABASE OF SYSTEMATIC REVIEWS, 1-120. doi:10.1002/14651858.CD009841.pub3

    DOI: 10.1002/14651858.CD009841.pub3

    Rethinking Strategies for Positive Newborn Screening Result (NBS+) Delivery (ReSPoND): a process evaluation of co-designing interventions to minimise impact on parental emotional well-being and stress. (Journal article)

    Chudleigh, J., Bonham, J., Bryon, M., Francis, J., Moody, L., Morris, S., . . . Southern, K. (2019). Rethinking Strategies for Positive Newborn Screening Result (NBS+) Delivery (ReSPoND): a process evaluation of co-designing interventions to minimise impact on parental emotional well-being and stress.. Pilot and feasibility studies, 5, 108. doi:10.1186/s40814-019-0487-5

    DOI: 10.1186/s40814-019-0487-5

    Impact of newborn screening on outcomes and social inequalities in cystic fibrosis: a UK CF registry-based study (Journal article)

    Schlüter, D. K., Southern, K. W., Dryden, C., Diggle, P., & Taylor-Robinson, D. (2020). Impact of newborn screening on outcomes and social inequalities in cystic fibrosis: a UK CF registry-based study. Thorax, 75(02), 123-131. doi:10.1136/thoraxjnl-2019-213179

    DOI: 10.1136/thoraxjnl-2019-213179

    2018

    SEROLOGICAL CLASSIFICATION OF ASPERGILLUS DISEASE IN CHILDHOOD (Conference Paper)

    Akinyemi, H. A., Mangat, S., Southern, K. W., Bedford, C., & McNamara, P. S. (2018). SEROLOGICAL CLASSIFICATION OF ASPERGILLUS DISEASE IN CHILDHOOD. In THORAX Vol. 73 (pp. A86-A87). doi:10.1136/thorax-2018-212555.145

    DOI: 10.1136/thorax-2018-212555.145

    A formative study exploring perceptions of physical activity and physical activity monitoring among children and young people with cystic fibrosis and health care professionals (Journal article)

    Shelley, J., Fairclough, S. J., Knowles, Z. R., Southern, K. W., McCormack, P., Dawson, E. A., . . . Hanlon, C. (2018). A formative study exploring perceptions of physical activity and physical activity monitoring among children and young people with cystic fibrosis and health care professionals. BMC PEDIATRICS, 18. doi:10.1186/s12887-018-1301-x

    DOI: 10.1186/s12887-018-1301-x

    THE IMPACT OF NEWBORN SCREENING ON OUTCOMES AND INEQUALITIES IN CYSTIC FIBROSIS: A UK REGISTRY BASED STUDY (Conference Paper)

    Schluter, D. K., Dryden, C., Southern, K. W., Diggle, P. J., & Taylor-Robinson, D. (2018). THE IMPACT OF NEWBORN SCREENING ON OUTCOMES AND INEQUALITIES IN CYSTIC FIBROSIS: A UK REGISTRY BASED STUDY. In JOURNAL OF EPIDEMIOLOGY AND COMMUNITY HEALTH Vol. 72 (pp. A27). doi:10.1136/jech-2018-SSMabstracts.55

    DOI: 10.1136/jech-2018-SSMabstracts.55

    Correctors (specific therapies for class II CFTR mutations) for cystic fibrosis (Journal article)

    Southern, K. W., Patel, S., Sinha, I. P., & Nevitt, S. J. (2018). Correctors (specific therapies for class II CFTR mutations) for cystic fibrosis. Cochrane Database of Systematic Reviews. doi:10.1002/14651858.CD010966.pub2

    DOI: 10.1002/14651858.CD010966.pub2

    ECFS best practice guidelines: the 2018 revision (Journal article)

    Castellani, C., Duff, A. J. A., Bell, S. C., Heijerman, H. G. M., Munck, A., Ratjen, F., . . . Drevinek, P. (2018). ECFS best practice guidelines: the 2018 revision. JOURNAL OF CYSTIC FIBROSIS, 17(2), 153-178. doi:10.1016/j.jcf.2018.02.006

    DOI: 10.1016/j.jcf.2018.02.006

    2017

    Autogenic drainage for airway clearance in cystic fibrosis (Journal article)

    McCormack, P., Burnham, P., & Southern, K. W. (2017). Autogenic drainage for airway clearance in cystic fibrosis. COCHRANE DATABASE OF SYSTEMATIC REVIEWS, (10). doi:10.1002/14651858.CD009595.pub2

    DOI: 10.1002/14651858.CD009595.pub2

    Real life practice of sweat testing in Europe (Journal article)

    Cirilli, N., Southern, K. W., Buzzetti, R., Barben, J., Nahrlich, L., Munck, A., . . . Working, E. C. F. S. D. N. (2018). Real life practice of sweat testing in Europe. JOURNAL OF CYSTIC FIBROSIS, 17(3), 325-332. doi:10.1016/j.jcf.2017.09.002

    DOI: 10.1016/j.jcf.2017.09.002

    A mixed methods study of the administration of flucloxacillin oral liquid; identifying strategies to overcome administration issues of medicines with poor palatability. (Journal article)

    Rouse, C., Mistry, P., Rayner, O., Nickless, J., Wan, M., Southern, K. W., & Batchelor, H. K. (2017). A mixed methods study of the administration of flucloxacillin oral liquid; identifying strategies to overcome administration issues of medicines with poor palatability.. The International journal of pharmacy practice, 25(5), 326-334. doi:10.1111/ijpp.12308

    DOI: 10.1111/ijpp.12308

    Ataluren and similar compounds (specific therapies for premature termination codon class I mutations) for cystic fibrosis (Journal article)

    Aslam, A., Jahnke, N., Remmington, T., & Southern, K. W. (2017). Ataluren and similar compounds (specific therapies for premature termination codon class I mutations) for cystic fibrosis. PAEDIATRIC RESPIRATORY REVIEWS, 24, 32-34. doi:10.1016/j.prrv.2017.04.001

    DOI: 10.1016/j.prrv.2017.04.001

    Investigating the variation in the incidence of new Pseudomonas aeruginosa infection between paediatric cystic fibrosis centres. (Journal article)

    Gilchrist, F. J., Jones, A. M., Smyth, A. R., Southern, K. W., Webb, A. K., & Lenney, W. (2017). Investigating the variation in the incidence of new Pseudomonas aeruginosa infection between paediatric cystic fibrosis centres.. Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society, 16(5), e14-e16. doi:10.1016/j.jcf.2017.06.006

    DOI: 10.1016/j.jcf.2017.06.006

    The expansion and performance of national newborn screening programmes for cystic fibrosis in Europe. (Journal article)

    Barben, J., Castellani, C., Dankert-Roelse, J., Gartner, S., Kashirskaya, N., Linnane, B., . . . Southern, K. W. (2017). The expansion and performance of national newborn screening programmes for cystic fibrosis in Europe. JOURNAL OF CYSTIC FIBROSIS, 16(2), 207-213. doi:10.1016/j.jcf.2016.12.012

    DOI: 10.1016/j.jcf.2016.12.012

    Topical cystic fibrosis transmembrane conductance regulator gene replacement for cystic fibrosis-related lung disease (Journal article)

    Perry, L. A., Penny-Dimri, J. C., Aslam, A. A., Lee, T. W., & Southern, K. W. (2017). Topical cystic fibrosis transmembrane conductance regulator gene replacement for cystic fibrosis-related lung disease. PAEDIATRIC RESPIRATORY REVIEWS, 22, 47-49. doi:10.1016/j.prrv.2016.10.005

    DOI: 10.1016/j.prrv.2016.10.005

    Topical cystic fibrosis transmembrane conductance regulator gene replacement for cystic fibrosis-related lung disease. (Journal article)

    Perry, L. A., Penny-Dimri, J. C., Aslam, A. A., Lee, T. W., & Southern, K. W. (2017). Topical cystic fibrosis transmembrane conductance regulator gene replacement for cystic fibrosis-related lung disease.. Paediatric respiratory reviews, 22, 47-49. doi:10.1016/j.prrv.2016.10.005

    DOI: 10.1016/j.prrv.2016.10.005

    Cystic Fibrosis Transmembrane Conductance Regulator-Related Metabolic Syndrome and Cystic Fibrosis Screen Positive, Inconclusive Diagnosis. (Journal article)

    Ren, C. L., Borowitz, D. S., Gonska, T., Howenstine, M. S., Levy, H., Massie, J., . . . Southern, K. W. (2017). Cystic Fibrosis Transmembrane Conductance Regulator-Related Metabolic Syndrome and Cystic Fibrosis Screen Positive, Inconclusive Diagnosis. JOURNAL OF PEDIATRICS, 181, S45-+. doi:10.1016/j.jpeds.2016.09.066

    DOI: 10.1016/j.jpeds.2016.09.066

    Diagnosis of Cystic Fibrosis: Consensus Guidelines from the Cystic Fibrosis Foundation. (Journal article)

    Farrell, P. M., White, T. B., Ren, C. L., Hempstead, S. E., Accurso, F., Derichs, N., . . . Sosnay, P. R. (2017). Diagnosis of Cystic Fibrosis: Consensus Guidelines from the Cystic Fibrosis Foundation. JOURNAL OF PEDIATRICS, 181, S4-S15. doi:10.1016/j.jpeds.2016.09.064

    DOI: 10.1016/j.jpeds.2016.09.064

    Ataluren and similar compounds (specific therapies for premature termination codon class I mutations) for cystic fibrosis (Journal article)

    Aslam, A. A., Higgins, C., Sinha, I. P., & Southern, K. W. (2017). Ataluren and similar compounds (specific therapies for premature termination codon class I mutations) for cystic fibrosis. Cochrane Database of Systematic Reviews. doi:10.1002/14651858.cd012040

    DOI: 10.1002/14651858.cd012040

    Ataluren and similar compounds (specific therapies for premature termination codon class I mutations) for cystic fibrosis. (Journal article)

    Aslam, A. A., Higgins, C., Sinha, I. P., & Southern, K. W. (2017). Ataluren and similar compounds (specific therapies for premature termination codon class I mutations) for cystic fibrosis.. The Cochrane database of systematic reviews, (1), 1-20. doi:10.1002/14651858.cd012040.pub2

    DOI: 10.1002/14651858.cd012040.pub2

    2016

    Antifungal therapies for allergic bronchopulmonary aspergillosis in people with cystic fibrosis (Journal article)

    Elphick, H. E., & Southern, K. W. (2016). Antifungal therapies for allergic bronchopulmonary aspergillosis in people with cystic fibrosis. COCHRANE DATABASE OF SYSTEMATIC REVIEWS, (11). doi:10.1002/14651858.CD002204.pub4

    DOI: 10.1002/14651858.CD002204.pub4

    Cystic fibrosis screen positive, inconclusive diagnosis (Journal article)

    Barben, J., & Southern, K. W. (2016). Cystic fibrosis screen positive, inconclusive diagnosis. CURRENT OPINION IN PULMONARY MEDICINE, 22(6), 617-622. doi:10.1097/MCP.0000000000000314

    DOI: 10.1097/MCP.0000000000000314

    Pneumococcal vaccines for cystic fibrosis (Journal article)

    Burgess, L., & Southern, K. W. (2016). Pneumococcal vaccines for cystic fibrosis. COCHRANE DATABASE OF SYSTEMATIC REVIEWS, (9). doi:10.1002/14651858.CD008865.pub4

    DOI: 10.1002/14651858.CD008865.pub4

    Newborn screening for cystic fibrosis (Journal article)

    Castellani, C., Massie, J., Sontag, M., & Southern, K. W. (2016). Newborn screening for cystic fibrosis. The Lancet Respiratory Medicine, 4(8), 653-661. doi:10.1016/S2213-2600(16)00053-9

    DOI: 10.1016/S2213-2600(16)00053-9

    Topical cystic fibrosis transmembrane conductance regulator gene replacement for cystic fibrosis-related lung disease (Journal article)

    Lee, T. W. R., Southern, K. W., Perry, L. A., Penny-Dimri, J. C., & Aslam, A. A. (2016). Topical cystic fibrosis transmembrane conductance regulator gene replacement for cystic fibrosis-related lung disease. COCHRANE DATABASE OF SYSTEMATIC REVIEWS, (6). doi:10.1002/14651858.CD005599.pub5

    DOI: 10.1002/14651858.CD005599.pub5

    Safety, pharmacokinetics, and pharmacodynamics of ivacaftor in patients aged 2-5 years with cystic fibrosis and a CFTR gating mutation (KIWI): an open-label, single-arm study (Journal article)

    Davies, J. C., Cunningham, S., Harris, W. T., Lapey, A., Regelmann, W. E., Sawicki, G. S., . . . Grp, K. I. W. I. S. (2016). Safety, pharmacokinetics, and pharmacodynamics of ivacaftor in patients aged 2-5 years with cystic fibrosis and a CFTR gating mutation (KIWI): an open-label, single-arm study. LANCET RESPIRATORY MEDICINE, 4(2), 107-115. doi:10.1016/S2213-2600(15)00545-7

    DOI: 10.1016/S2213-2600(15)00545-7

    2015

    IVACAFTOR TREATMENT IN PRESCHOOL CHILDREN WITH CYSTIC FIBROSIS AND A CFTR GATING MUTATION: EXTENDED EVALUATION (Conference Paper)

    Davies, J. C., Cunningham, S., Southern, K. W., Robertson, S., Green, Y., Cooke, J., . . . Rosenfeld, M. (2015). IVACAFTOR TREATMENT IN PRESCHOOL CHILDREN WITH CYSTIC FIBROSIS AND A CFTR GATING MUTATION: EXTENDED EVALUATION. In THORAX Vol. 70 (pp. A14). doi:10.1136/thoraxjnl-2015-207770.24

    DOI: 10.1136/thoraxjnl-2015-207770.24

    Cystic Fibrosis Screen Positive, Inconclusive Diagnosis (CFSPID): A new designation and management recommendations for infants with an inconclusive diagnosis following newborn screening (Journal article)

    Munck, A., Mayell, S. J., Winters, V., Shawcross, A., Derichs, N., Parad, R., . . . Southern, K. W. (2015). Cystic Fibrosis Screen Positive, Inconclusive Diagnosis (CFSPID): A new designation and management recommendations for infants with an inconclusive diagnosis following newborn screening. Journal of Cystic Fibrosis, 14(6), 706-713. doi:10.1016/j.jcf.2015.01.001

    DOI: 10.1016/j.jcf.2015.01.001

    Exhaled breath hydrogen cyanide as a marker of early Pseudomonas aeruginosa infection in children with cystic fibrosis. (Journal article)

    Gilchrist, F. J., Belcher, J., Jones, A. M., Smith, D., Smyth, A. R., Southern, K. W., . . . Lenney, W. (2015). Exhaled breath hydrogen cyanide as a marker of early Pseudomonas aeruginosa infection in children with cystic fibrosis.. ERJ open research, 1(2). doi:10.1183/23120541.00044-2015

    DOI: 10.1183/23120541.00044-2015

    PERFORMANCE OF THE UK NEWBORN SCREENING PROGRAMME FOR CF, WHICH INCORPORATES STRATEGIES TO IMPROVE POSITIVE PREDICTIVE VALUE AND REDUCE CARRIER RECOGNITION (Journal article)

    Southern, K. W., Morgan, T., Kour, S., Scott, E., Coppinger, C., Cavanagh, C., . . . Price, J. (2015). PERFORMANCE OF THE UK NEWBORN SCREENING PROGRAMME FOR CF, WHICH INCORPORATES STRATEGIES TO IMPROVE POSITIVE PREDICTIVE VALUE AND REDUCE CARRIER RECOGNITION. PEDIATRIC PULMONOLOGY, 50, 382-383. Retrieved from http://gateway.webofknowledge.com/

    Social network analysis of Pseudomonas aeruginosa in cystic fibrosis (Journal article)

    Taylor-Robinson, D. C., Southern, K. W., & Winstanley, C. (2015). Social network analysis of Pseudomonas aeruginosa in cystic fibrosis. LANCET RESPIRATORY MEDICINE, 3(8), 595-596. doi:10.1016/S2213-2600(15)00250-7

    DOI: 10.1016/S2213-2600(15)00250-7

    Topical nasal steroids for treating nasal polyposis in people with cystic fibrosis (Journal article)

    Beer, H., Southern, K. W., & Swift, A. C. (2015). Topical nasal steroids for treating nasal polyposis in people with cystic fibrosis. COCHRANE DATABASE OF SYSTEMATIC REVIEWS, (6). doi:10.1002/14651858.CD008253.pub4

    DOI: 10.1002/14651858.CD008253.pub4

    Potentiators (specific therapies for class III and IV mutations) for cystic fibrosis (Journal article)

    Patel, S., Sinha, I. P., Dwan, K., Echevarria, C., Schechter, M., & Southern, K. W. (2015). Potentiators (specific therapies for class III and IV mutations) for cystic fibrosis. COCHRANE DATABASE OF SYSTEMATIC REVIEWS, (03), 1-91. doi:10.1002/14651858.CD009841.pub2

    DOI: 10.1002/14651858.CD009841.pub2

    Potentiators for cystic fibrosis - targeting the underlying molecular defect (Journal article)

    Patel, S., Sinha, I. P., Dwan, K., Echevarria, C., Schechter, M., & Southern, K. W. (2015). Potentiators for cystic fibrosis - targeting the underlying molecular defect. PAEDIATRIC RESPIRATORY REVIEWS, 16(3), 162-164. doi:10.1016/j.prrv.2015.04.003

    DOI: 10.1016/j.prrv.2015.04.003

    2014

    THE INCIDENCE OF NEW PSEUDOMONAS AERUGINOSA INFECTION IN CHILDREN WITH CYSTIC FIBROSIS (Conference Paper)

    Gilchrist, F. J., Belcher, J., Jones, A. M., Smith, D., Smyth, A., Southern, K. W., . . . Lenney, W. (2014). THE INCIDENCE OF NEW PSEUDOMONAS AERUGINOSA INFECTION IN CHILDREN WITH CYSTIC FIBROSIS. In THORAX Vol. 69 (pp. A162-A163). doi:10.1136/thoraxjnl-2014-206260.326

    DOI: 10.1136/thoraxjnl-2014-206260.326

    Antifungal therapies for allergic bronchopulmonary aspergillosis in people with cystic fibrosis (Journal article)

    Elphick, H. E., & Southern, K. W. (2014). Antifungal therapies for allergic bronchopulmonary aspergillosis in people with cystic fibrosis. COCHRANE DATABASE OF SYSTEMATIC REVIEWS, (11). doi:10.1002/14651858.CD002204.pub3

    DOI: 10.1002/14651858.CD002204.pub3

    Pneumococcal vaccines for cystic fibrosis (Journal article)

    Burgess, L., & Southern, K. W. (2014). Pneumococcal vaccines for cystic fibrosis. COCHRANE DATABASE OF SYSTEMATIC REVIEWS, (8). doi:10.1002/14651858.CD008865.pub3

    DOI: 10.1002/14651858.CD008865.pub3

    THE B LYMPHOCYTE DIFFERENTIATION FACTOR (BAFF) IS EXPRESSED IN THE AIRWAYS OF CHILDREN WITH CF AND IN LUNGS OF MICE INFECTED WITH PSEUDOMONAS AERUGINOSA (Journal article)

    Neill, D. R., Saint, G. L., Bricio-Moreno, L., Fothergill, J., Southern, K. W., Winstanley, C., . . . Flanagan, B. F. (2014). THE B LYMPHOCYTE DIFFERENTIATION FACTOR (BAFF) IS EXPRESSED IN THE AIRWAYS OF CHILDREN WITH CF AND IN LUNGS OF MICE INFECTED WITH PSEUDOMONAS AERUGINOSA. PLoS One, 9(5). doi:10.1371/journal.pone.0095892.

    DOI: 10.1371/journal.pone.0095892.

    European Cystic Fibrosis Society Standards of Care: Best Practice guidelines (Journal article)

    Smyth, A. R., Bell, S. C., Bojcin, S., Bryon, M., Duff, A., Flume, P., . . . Wolfe, S. (2014). European Cystic Fibrosis Society Standards of Care: Best Practice guidelines. JOURNAL OF CYSTIC FIBROSIS, 13(Supplement 1), S23-S42. doi:10.1016/j.jcf.2014.03.010

    DOI: 10.1016/j.jcf.2014.03.010

    Sodium channel blockers for cystic fibrosis. (Journal article)

    Burrows, E. F., Southern, K. W., & Noone, P. G. (2014). Sodium channel blockers for cystic fibrosis.. The Cochrane database of systematic reviews, (4), CD005087. doi:10.1002/14651858.cd005087.pub4

    DOI: 10.1002/14651858.cd005087.pub4

    Considering consent: a structural equation modelling analysis of factors influencing decisional quality when accepting newborn screening (Journal article)

    Nicholls, S. G., & Southern, K. W. (2014). Considering consent: a structural equation modelling analysis of factors influencing decisional quality when accepting newborn screening. JOURNAL OF INHERITED METABOLIC DISEASE, 37(2), 197-205. doi:10.1007/s10545-013-9651-x

    DOI: 10.1007/s10545-013-9651-x

    Correctors (specific therapies for class II CFTR mutations) for cystic fibrosis (Journal article)

    Sinha, I. P., Southern, K. W., Dwan, K., & Patel, S. (n.d.). Correctors (specific therapies for class II CFTR mutations) for cystic fibrosis. Cochrane Database of Systematic Reviews. doi:10.1002/14651858.cd010966

    DOI: 10.1002/14651858.cd010966

    Gastrointestinal surgery in cystic fibrosis: A 20-year review (Journal article)

    Farrelly, P. J., Charlesworth, C., Lee, S., Southern, K. W., & Baillie, C. T. (2014). Gastrointestinal surgery in cystic fibrosis: A 20-year review. JOURNAL OF PEDIATRIC SURGERY, 49(2), 280-283. doi:10.1016/j.jpedsurg.2013.11.038

    DOI: 10.1016/j.jpedsurg.2013.11.038

    Newborn screening for cystic fibrosis: opportunities and remaining challenges (Journal article)

    Mehta, A., Sommerburg, O., & Southern, K. W. (2014). Newborn screening for cystic fibrosis: opportunities and remaining challenges. Unknown Journal, 65-76. doi:10.1183/1025448x.10008913

    DOI: 10.1183/1025448x.10008913

    The challenge of improving outcomes for patients with CF sinonasal disease (Journal article)

    VanDevanter, D. R., & Southern, K. W. (2014). The challenge of improving outcomes for patients with CF sinonasal disease. JOURNAL OF CYSTIC FIBROSIS, 13(4), 361-362. doi:10.1016/j.jcf.2014.05.014

    DOI: 10.1016/j.jcf.2014.05.014

    Turnover of strains and intraclonal variation amongst Pseudomonas aeruginosa isolates from paediatric CF patients (Journal article)

    Hall, A. J., Fothergill, J. L., McNamara, P. S., Southern, K. W., & Winstanley, C. (2014). Turnover of strains and intraclonal variation amongst Pseudomonas aeruginosa isolates from paediatric CF patients. DIAGNOSTIC MICROBIOLOGY AND INFECTIOUS DISEASE, 80(4), 324-326. doi:10.1016/j.diagmicrobio.2014.09.007

    DOI: 10.1016/j.diagmicrobio.2014.09.007

    Variations in inflammation-related genes may be associated with childhood febrile seizure susceptibility (Journal article)

    Emsley, H. C. A., Appleton, R. E., Whitmore, C. L., Jury, F., Lamb, J. A., Martin, J. E., . . . Allan, S. M. (2014). Variations in inflammation-related genes may be associated with childhood febrile seizure susceptibility. SEIZURE-EUROPEAN JOURNAL OF EPILEPSY, 23(6), 457-461. doi:10.1016/j.seizure.2014.03.006

    DOI: 10.1016/j.seizure.2014.03.006

    2013

    Comparison of real time diagnostic chemistries to detect Pseudomonas aeruginosa in respiratory samples from cystic fibrosis patients (Journal article)

    Fothergill, J. L., Ledson, M. J., Walshaw, M. J., McNamara, P. S., Southern, K. W., & Winstanley, C. (2013). Comparison of real time diagnostic chemistries to detect Pseudomonas aeruginosa in respiratory samples from cystic fibrosis patients. JOURNAL OF CYSTIC FIBROSIS, 12(6), 675-681. doi:10.1016/j.jcf.2013.04.007

    DOI: 10.1016/j.jcf.2013.04.007

    Abnormal tracheal smooth muscle function in the CF mouse (Journal article)

    Wallace, H. L., Southern, K. W., Connell, M. G., Wray, S., & Burdyga, T. (2013). Abnormal tracheal smooth muscle function in the CF mouse. Physiological Reports, 1(6). doi:10.1002/phy2.138

    DOI: 10.1002/phy2.138

    Adherence to nebulised therapies in adolescents with cystic fibrosis is best on week-days during school term-time (Journal article)

    Ball, R., Southern, K. W., McCormack, P., Duff, A. J. A., Brownlee, K. G., & McNamara, P. S. (2013). Adherence to nebulised therapies in adolescents with cystic fibrosis is best on week-days during school term-time. JOURNAL OF CYSTIC FIBROSIS, 12(5), 440-444. doi:10.1016/j.jcf.2012.12.012

    DOI: 10.1016/j.jcf.2012.12.012

    Intraclonal genetic diversity amongst cystic fibrosis and keratitis isolates of Pseudomonas aeruginosa. (Journal article)

    Hall, A. J., Fothergill, J. L., Kaye, S. B., Neal, T. J., McNamara, P. S., Southern, K. W., & Winstanley, C. (2013). Intraclonal genetic diversity amongst cystic fibrosis and keratitis isolates of Pseudomonas aeruginosa.. Journal of medical microbiology, 62(Pt 2), 208-216. doi:10.1099/jmm.0.048272-0

    DOI: 10.1099/jmm.0.048272-0

    After a long wait, two arrive, one after the other! (Journal article)

    Southern, K. W., McCormack, P., & McNamara, P. S. (2013). After a long wait, two arrive, one after the other!. THORAX, 68(4), 311-312. doi:10.1136/thoraxjnl-2012-202891

    DOI: 10.1136/thoraxjnl-2012-202891

    Intraclonal genetic diversity amongst cystic fibrosis and keratitis isolates of Pseudomonas aeruginosa (Journal article)

    Hall, A. J., Fothergill, J. L., Kaye, S. B., Neal, T. J., McNamara, P. S., Southern, K. W., & Winstanley, C. (2013). Intraclonal genetic diversity amongst cystic fibrosis and keratitis isolates of Pseudomonas aeruginosa. Journal of Medical Microbiology, 62, 208-216.

    2012

    New Nebulizer Technology to Monitor Adherence and Nebulizer Performance in Cystic Fibrosis (Journal article)

    McCormack, P., Southern, K. W., & McNamara, P. S. (2012). New Nebulizer Technology to Monitor Adherence and Nebulizer Performance in Cystic Fibrosis. JOURNAL OF AEROSOL MEDICINE AND PULMONARY DRUG DELIVERY, 25(6), 307-309. doi:10.1089/jamp.2011.0934

    DOI: 10.1089/jamp.2011.0934

    Assessing the Liverpool Respiratory Symptom Questionnaire in children with cystic fibrosis (Journal article)

    Trinick, R., Southern, K. W., & McNamara, P. S. (2012). Assessing the Liverpool Respiratory Symptom Questionnaire in children with cystic fibrosis. EUROPEAN RESPIRATORY JOURNAL, 39(4), 899-905. doi:10.1183/09031936.00070311

    DOI: 10.1183/09031936.00070311

    Mutation-specific therapies that potentiate cystic fibrosis transmembrane conductance regulator (CFTR) function in cystic fibrosis (Journal article)

    Sinha, I. P., Southern, K. W., Dwan, K., Echevarria, C., & Schechter, M. (n.d.). Mutation-specific therapies that potentiate cystic fibrosis transmembrane conductance regulator (CFTR) function in cystic fibrosis. doi:10.1002/14651858.cd009841

    DOI: 10.1002/14651858.cd009841

    2011

    Poster Session Abstracts (Journal article)

    Poster Session Abstracts (2011). Pediatric Pulmonology, 46(S34), 212-428. doi:10.1002/ppul.21583

    DOI: 10.1002/ppul.21583

    A randomised controlled trial of breathing modes for adaptive aerosol delivery in children with cystic fibrosis (Journal article)

    McCormack, P., McNamara, P. S., & Southern, K. W. (2011). A randomised controlled trial of breathing modes for adaptive aerosol delivery in children with cystic fibrosis. JOURNAL OF CYSTIC FIBROSIS, 10(5), 343-349. doi:10.1016/j.jcf.2011.04.006

    DOI: 10.1016/j.jcf.2011.04.006

    Array tube genotyping of Pseudomonas aeruginosa isolates as a strategy for identifying potential emerging transmissible strains. (Journal article)

    Hall, A. J., Fothergill, J. L., Southern, K. W., McNamara, P. S., Ledson, M. J., Walshaw, M. J., & Winstanley, C. (2011). Array tube genotyping of Pseudomonas aeruginosa isolates as a strategy for identifying potential emerging transmissible strains.. Journal of Cystic Fibrosis, 10 (S1, S32.

    Comparison of real time diagnostic chemistries to detect early and chronic Pseudomonas aeruginosa colonisation in cystic fibrosis patients (Journal article)

    Fothergill, J. L., Walshaw, M. J., Ledson, M. J., Southern, K. W., McNamara, P. S., & Winstanley, C. (2011). Comparison of real time diagnostic chemistries to detect early and chronic Pseudomonas aeruginosa colonisation in cystic fibrosis patients. Journal of Cystic Fibrosis, 10 (S1, S32.

    Macrolide antibiotics for cystic fibrosis (Journal article)

    Southern, K. W., Barker, P. M., Solis-Moya, A., & Patel, L. (2011). Macrolide antibiotics for cystic fibrosis. Cochrane Database of Systematic Reviews.

    2010

    "Guidelines on the early management of infants diagnosed with cystic fibrosis following newborn screening" (Journal article)

    Sermet-Gaudelus, I., Mayell, S., & Southern, K. W. (2010). "Guidelines on the early management of infants diagnosed with cystic fibrosis following newborn screening". Journal of Cystic Fibrosis, 9(5), 323-329.

    Components of risk associated with home intravenous antibiotic therapy (H-IVAT) in the UK (Journal article)

    Glasscoe, C., Quittner, A. L., Dale, C., Patel, L., Burrows, E. F., Hope, H. F., . . . Nunn, A. J. (2010). Components of risk associated with home intravenous antibiotic therapy (H-IVAT) in the UK. Journal of Cystic Fibrosis, 9, S105.

    Microarray genotyping of Pseudomonas aeruginosa isolates from CF units. (Journal article)

    Hall, A. J., Fothergill, J. L., Southern, K. W., McNamara, P. S., Ledson, M. J., Walshaw, M. J., & Winstanley, C. (2010). Microarray genotyping of Pseudomonas aeruginosa isolates from CF units.. Journal of Cystic Fibrosis, 9(S1), S30.

    2009

    Open adherence monitoring using routine data download from an adaptive aerosol delivery nebuliser in children with cystic fibrosis (Journal article)

    McNamara, P. S., McCormack, P., McDonald, A. J., Heaf, L., & Southern, K. W. (2009). Open adherence monitoring using routine data download from an adaptive aerosol delivery nebuliser in children with cystic fibrosis. JOURNAL OF CYSTIC FIBROSIS, 8(4), 258-263. doi:10.1016/j.jcf.2009.04.006

    DOI: 10.1016/j.jcf.2009.04.006

    European best practice guidelines for cystic fibrosis neonatal screening (Journal article)

    Castellani, C., Southern, K. W., Brownlee, K., Dankert Roelse, J., Duff, A., Farrell, M., . . . Elborn, S. (2009). European best practice guidelines for cystic fibrosis neonatal screening. Journal of Cystic Fibrosis, 8(3), 153-173. doi:10.1016/j.jcf.2009.01.004

    DOI: 10.1016/j.jcf.2009.01.004

    A European consensus for the evaluation and management of infants with an equivocal diagnosis following newborn screening for cystic fibrosis (Journal article)

    Mayell, S. J., Munck, A., Craig, J. V., Sermet, I., Brownlee, K. G., Schwarz, M. J., . . . Southern, K. W. (2009). A European consensus for the evaluation and management of infants with an equivocal diagnosis following newborn screening for cystic fibrosis. Journal of Cystic Fibrosis, 8(1), 71-78. doi:10.1016/j.jcf.2008.09.005

    DOI: 10.1016/j.jcf.2008.09.005

    A reducing prevalence of the Liverpool Epidemic Strain of Pseudomonas aeruginosa in children attending the index paediatric clinic. (Journal article)

    Morris, D., Fallon, L., Heaf, L., Burrows, E. F., Wallace, H., McNamara, P. S., . . . Southern, K. W. (2009). A reducing prevalence of the Liverpool Epidemic Strain of Pseudomonas aeruginosa in children attending the index paediatric clinic.. Ped Pulmonol, 32, 325.

    A reducing prevalence of the Liverpool Epidemic Strain of Pseudomonas aeruginosa in children attending the index paediatric clinic. (Journal article)

    Morris, D., Fallon, L., Heaf, L., Burrows, E. F., Wallace, H., McNamara, P. N., . . . Southern, K. W. (2009). A reducing prevalence of the Liverpool Epidemic Strain of Pseudomonas aeruginosa in children attending the index paediatric clinic.. Pediatric Pulmonology, S32, 325.

    A reference interval for sweat chloride in infants aged between five and six weeks of age (Journal article)

    Jayaraj, R., Barton, P. V., Newland, P., Mountford, R., Shaw, N. J., Mccarthy, E., . . . Southern, K. W. (2009). A reference interval for sweat chloride in infants aged between five and six weeks of age. Annals of Clinical Biochemistry: International Journal of Laboratory Medicine, 46(1), 73-78. doi:10.1258/acb.2008.008081

    DOI: 10.1258/acb.2008.008081

    Estimating risk associated with home-based intravenous antibiotic therapy (IVAT) (Journal article)

    Glasscoe, C., Southern, K. W., Lancaster, G. A., Quittner, A. L., Burrows, E., Heaf, L., . . . Nunn, A. J. (2009). Estimating risk associated with home-based intravenous antibiotic therapy (IVAT). Journal of Cystic Fibrosis, 8, S95.

    Newborn screening for cystic fibrosis (Journal article)

    Southern, K. W., Merelle, M. M., Dankert-Roelse, J. E., & Nagelkerke, A. D. (2009). Newborn screening for cystic fibrosis. Cochrane database of systematic reviews.

    Phenotypic characterization of patients with intermediate sweat chloride values: towards validation of the European diagnostic algorithm for cystic fibrosis (Journal article)

    Goubau, C., Wilschanski, M., & al., E. (2009). Phenotypic characterization of patients with intermediate sweat chloride values: towards validation of the European diagnostic algorithm for cystic fibrosis. Thorax. Retrieved from http://www.ncbi.nlm.nih.gov/

    2008

    Embryonic lung growth is normal in a cftr-knockout mouse model. (Journal article)

    Wallace, H. L., Connell, M. G., Losty, P. D., Jesudason, E. C., & Southern, K. W. (2008). Embryonic lung growth is normal in a cftr-knockout mouse model.. Experimental lung research, 34(10), 717-727. doi:10.1080/01902140802389719

    DOI: 10.1080/01902140802389719

    Airway ion transport impacts on disease presentation and severity in cystic fibrosis (Journal article)

    Leal, T., Fajac, I., Wallace, H. L., Lebecque, P., Lebacq, J., Hubert, D., . . . Southern, K. W. (2008). Airway ion transport impacts on disease presentation and severity in cystic fibrosis. Clinical Biochemistry, 41(10-11), 764-772. doi:10.1016/j.clinbiochem.2008.03.013

    DOI: 10.1016/j.clinbiochem.2008.03.013

    Challenge of Living with Cystic Fibrosis (CLCF): Psychometric evaluation (Conference Paper)

    Glasscoe, C., Southern, K. W., Hope, H. F., Burrows, E., Heaf, L., Brownlee, K., . . . Quittner, A. L. (2008). Challenge of Living with Cystic Fibrosis (CLCF): Psychometric evaluation. In European CF Conference (pp. S96). Prague: Journal of Cystic Fibrosis.

    2007

    Less is best? The impact of urokinase as the first line management of empyema thoracis. (Journal article)

    Khalil, B. A., Corbett, P. A., Jones, M. O., Baillie, C. T., Southern, K., Losty, P. D., & Kenny, S. E. (2007). Less is best? The impact of urokinase as the first line management of empyema thoracis.. Pediatric surgery international, 23(2), 129-133. doi:10.1007/s00383-006-1806-5

    DOI: 10.1007/s00383-006-1806-5

    A survey of newborn screening for cystic fibrosis in Europe (Journal article)

    Southern, K. W., Munck, A., Pollitt, R., Travert, G., Zanolla, L., Dankert-Roelse, J., & Castellani, C. (2007). A survey of newborn screening for cystic fibrosis in Europe. Journal of Cystic Fibrosis, 6(1), 57-65. doi:10.1016/j.jcf.2006.05.008

    DOI: 10.1016/j.jcf.2006.05.008

    Achieving sustained compliance with nebulised therapies in a paediatric CF population (Journal article)

    McCormack, P., MacDonald, A., Southern, K. S., & McNamara, P. S. (2007). Achieving sustained compliance with nebulised therapies in a paediatric CF population. Journal of Cystic Fibrosis, 6(June), S67.

    Challenges of Living with Cystic Fibosis (CLCF): Psychometric evaluation of a new measure (Journal article)

    Glasscoe, C., Southern, K. W., Smith, J. A., Lancaster, G. A., Hill, J., Burrows, E. F., . . . Quittner, A. L. (2007). Challenges of Living with Cystic Fibosis (CLCF): Psychometric evaluation of a new measure. Pediatric Pulmonology, 30(Supp), 403.

    Electrical Potential Difference Across the Nasal Epithelium Is Reduced in Premature Infants With Chronic Lung Disease but Is Not Associated With Lower Airway Inflammation (Journal article)

    Gaillard, E. A., Shaw, N. J., Wallace, H. L., Vince, G., & Southern, K. W. (2007). Electrical Potential Difference Across the Nasal Epithelium Is Reduced in Premature Infants With Chronic Lung Disease but Is Not Associated With Lower Airway Inflammation. Pediatric Research, 61(1), 77-82. doi:10.1203/01.pdr.0000250035.10339.ce

    DOI: 10.1203/01.pdr.0000250035.10339.ce

    Living with Cystic Fibrosis Questionnaire (CFLC-Q): Development and preliminary validation of a new measure of the challenge experienced by caregivers (Journal article)

    Glasscoe, C., Quittner, A. L., Smith, J. A., Burrows, E. F., Heaf, L., Cottrell, J., . . . Lancaster, G. A. (2007). Living with Cystic Fibrosis Questionnaire (CFLC-Q): Development and preliminary validation of a new measure of the challenge experienced by caregivers. Journal of Cystic Fibrosis, 6(Supp 1), S76.

    Significant findings on cranial CT scan after a first unprovoked seizure in children from North India. (Journal article)

    Mathur, S., Southern, K., & Sharma, M. (2007). Significant findings on cranial CT scan after a first unprovoked seizure in children from North India.. Journal of Tropical Pediatrics, 56(6), 428-430.

    2006

    Pulmonary edema in meningococcal septicemia associated with reduced epithelial chloride transport (Journal article)

    Eisenhut, M., Wallace, H., Barton, P., Gaillard, E., Newland, P., Diver, M., & Southern, K. W. (2006). Pulmonary edema in meningococcal septicemia associated with reduced epithelial chloride transport. Pediatric Critical Care Medicine, 7(2), 119-124. doi:10.1097/01.pcc.0000200944.98424.e0

    DOI: 10.1097/01.pcc.0000200944.98424.e0

    A national survey of palivizumab for infants with cystic fibrosis (Journal article)

    McCormick, J., & Southern, K. W. (2006). A national survey of palivizumab for infants with cystic fibrosis. Paediatric Pulmonology, Supp., 431.

    A systematic (Cochrane) review of topical sodium channel blockers for cystic fibrosis lung disease (Journal article)

    Burrows, E. F., Noone, P. G., & Southern, K. W. (2006). A systematic (Cochrane) review of topical sodium channel blockers for cystic fibrosis lung disease. Paediatric Pulmonology, Supp., 355.

    Developing a tool to assess the impact on a family of caring for a child with cystic fibrosis (Journal article)

    Glasscoe, C., Quittner, A. L., Evans, J., Burrows, E. F., Cottrell, J. J., Heaf, L., . . . Southern, K. W. (2006). Developing a tool to assess the impact on a family of caring for a child with cystic fibrosis. Pediatric Pulmonology, 29, 405-406.

    Establishing paediatric patients on an Adaptive Aerosol Delivery (AAD) device (Journal article)

    McCormick, P., McDonald, A., & Southern, K. W. (2006). Establishing paediatric patients on an Adaptive Aerosol Delivery (AAD) device. Journal of Cystic Fibrosis, 5 (Sup, S76 (348).

    Reference range for sweat chloride in infants at 5-6 weeks of age (Journal article)

    Jayaraj, R., Newland, P., Barton, P., Shaw, N. J., Isherwood, D., & Southern, K. W. (2006). Reference range for sweat chloride in infants at 5-6 weeks of age. Paediatric Pulmonology, Supp., 547.

    The challenge of living with cystic fibrosis: A collective response from parents (Journal article)

    Glasscoe, C., Smith, J. A., Hope, H. F., Jones, S., Cottrell, J. J., Burrows, E. F., . . . Southern, K. W. (2006). The challenge of living with cystic fibrosis: A collective response from parents. Pediatric Pulmonology, 29, 406.

    Transition to adulthood for young people with CF (Journal article)

    Hogan, J., Horgan, M., Southern, K., Cotrell, J., & Burrows, E. (2006). Transition to adulthood for young people with CF. Journal of Cystic Fibrosis, 5 (Sup, S87 (393.

    Use of exacerbation score to determine intravenous antibiotic use for acute respiratory exacerbations in Cystic Fibrosis (Journal article)

    Das, D., Bako, O. L., Javadpour, S., Heaf, L. J., Southern, K. W., & Heaf, D. P. (2006). Use of exacerbation score to determine intravenous antibiotic use for acute respiratory exacerbations in Cystic Fibrosis. Journal of Cystic Fibrosis, 5 (Sup, S20 (91).

    Working in partnership with families to openly monitor aerosol therapy with an in-device data logger (Journal article)

    McCormack, P., McDonald, A., Couriel, J. M., & Southern, K. W. (2006). Working in partnership with families to openly monitor aerosol therapy with an in-device data logger. Journal of Cystic Fibrosis, 5 (sup, S77 (352).

    2005

    Nasal potential difference increases with gestation in moderately preterm neonates on the first postnatal day (Journal article)

    Gaillard, E. A. (2005). Nasal potential difference increases with gestation in moderately preterm neonates on the first postnatal day. Archives of Disease in Childhood - Fetal and Neonatal Edition, 90(2), F172-F173. doi:10.1136/adc.2004.054494

    DOI: 10.1136/adc.2004.054494

    A Survey on CF neonatal screening practice around Europe (Journal article)

    Castellani, C., Dankert-Roelse, J., Munck, A., Pollitt, R., Southern, K. W., & Travert, G. (2005). A Survey on CF neonatal screening practice around Europe. Journal of Cystic Fibrosis, 4, S130.

    Chloride channel dysfunction associated with pulmonary oedema in meningococcal septicaemia (Journal article)

    Eisenhut, M., Wallace, H. L., Barton, P., Gaillard, E., Newland, P., & Southern, K. W. (2005). Chloride channel dysfunction associated with pulmonary oedema in meningococcal septicaemia. Current Paediatrics, 15, 190-191.

    Does sputum induction (SI) increase recognition of an epidemic strain of Pseudomonas aeruginosa (PA)? (Journal article)

    Wallace, H. L., McCormack, P., Jeffers, G., Heaf, D. P., Winstanley, C., Hart, C. A., & Southern, K. W. (2005). Does sputum induction (SI) increase recognition of an epidemic strain of Pseudomonas aeruginosa (PA)?. Journal of Cystic Fibrosis, 4, S42.

    Once versus three-times daily regimens of tobramycin treatment for pulmonary exacerbations of cystic fibrosis--the TOPIC study: a randomised controlled trial. (Journal article)

    A, S., & et.al., F. T. T. S. G. (2005). Once versus three-times daily regimens of tobramycin treatment for pulmonary exacerbations of cystic fibrosis--the TOPIC study: a randomised controlled trial.. Lancet, 365(9459), 573-578. Retrieved from http://dx.doi.org/10.1016/S0140-6736(05)17906-9

    Sputum induction (SI) with 3% hypertonic saline in children (Journal article)

    McCormack, P., Wallace, H. L., Heaf, D. P., & Southern, K. W. (2005). Sputum induction (SI) with 3% hypertonic saline in children. Journal of Cystic Fibrosis, 4, S100.

    Suitability of the upper airway models obtained from MRI studies in simulating drug lung deposition from inhalers (Journal article)

    Ehtezazi, T., Southern, K. W., Allanson, D., Jenkinson, I., & O'Callaghan, C. (2005). Suitability of the upper airway models obtained from MRI studies in simulating drug lung deposition from inhalers. Pharm Res, 22, 166-170.

    Thyroid function during severe meningococcal disease (Journal article)

    Eisenhut, M., Newland, P., & Southern, K. W. (2005). Thyroid function during severe meningococcal disease. Pediatric Critical Care Medicine, 6, 239.

    2004

    Azithromycin for cystic fibrosis (Journal article)

    Southern, K. W., & Barker, P. M. (2004). Azithromycin for cystic fibrosis. Eur Respir J, 24(5), 834-838.

    Elevated sweat sodium associated with pulmonary oedema in meningococcal sepsis (Journal article)

    Eisenhut, M., Sidaras, D., Barton, P., Newland, P., & Southern, K. W. (2004). Elevated sweat sodium associated with pulmonary oedema in meningococcal sepsis. Eur J Clin Invest, 34, 834-838.

    2003

    Nasal Airway Ion Transport and Lung Function in Young People with Cystic Fibrosis (Journal article)

    Wallace, H. L., Barker, P. M., & Southern, K. W. (2003). Nasal Airway Ion Transport and Lung Function in Young People with Cystic Fibrosis. American Journal of Respiratory and Critical Care Medicine, 168(5), 594-600. doi:10.1164/rccm.200211-1302oc

    DOI: 10.1164/rccm.200211-1302oc

    Airway Ion Transport on the First Postnatal Day in Infants Delivered Vaginally or by Elective Cesarean Section (Journal article)

    Gaillard, E. A., Shaw, N. J., Wallace, H. L., Subhedar, N. V., & Southern, K. W. (2003). Airway Ion Transport on the First Postnatal Day in Infants Delivered Vaginally or by Elective Cesarean Section. Pediatric Research, 54(1), 58-63. doi:10.1203/01.pdr.0000069842.09976.cb

    DOI: 10.1203/01.pdr.0000069842.09976.cb

    Regulation of liquid secretion and absorption by the fetal and neonatal lung: basic mechanisms and role in neonatal lung disease (Chapter)

    Barker, P. M., & Southern, K. W. (2003). Regulation of liquid secretion and absorption by the fetal and neonatal lung: basic mechanisms and role in neonatal lung disease. In R. A. Polin, W. W. Fox, & S. H. Abman (Eds.), Fetal and Neonatal Physiology (pp. 822-834). Penn: Saunders.

    2002

    Airway Surface Liquid Recovered by Lavage with Perfluorocarbon Liquid in Cats (Journal article)

    Southern, K. W., Funkhouser, W. K., Kazachkova, I., Godfrey, V. L., Fordham, L. A., & Barker, P. M. (2002). Airway Surface Liquid Recovered by Lavage with Perfluorocarbon Liquid in Cats. Eur J Clin Invest, 32, 956-961.

    2001

    A modified technique for measurement of nasal transepithelial potential difference in infants (Journal article)

    Southern, K. W., Noone, P. G., Bosworth, D. G., LeGrys, V. A., Knowles, M. R., & Barker, P. M. (2001). A modified technique for measurement of nasal transepithelial potential difference in infants. The Journal of Pediatrics, 139(3), 353-358. doi:10.1067/mpd.2001.116278

    DOI: 10.1067/mpd.2001.116278

    1995

    Generation and characterization of a delta F508 cystic fibrosis mouse model. (Journal article)

    Colledge, W. H., Abella, B. S., Southern, K. W., Ratcliff, R., Jiang, C., Cheng, S. H., . . . Evans, M. J. (1995). Generation and characterization of a delta F508 cystic fibrosis mouse model.. Nature genetics, 10(4), 445-452. doi:10.1038/ng0895-445

    DOI: 10.1038/ng0895-445